Characteristics | Adult | Children | Total |
---|---|---|---|
Age in years, mean(SD) | Â | Â | 25.0 (9.8) |
Age, n(%) | |||
   ≤ 18 | - | 68(26.7%) |  |
   > 18 | 187(73.3%) | - |  |
Sex, n(%) | |||
  Male | 97(76.4%) | 30(23.6%) | 127(49.8%) |
  Female | 90 (70.3%) | 38(29.7%) | 128(50.2%) |
Household annual income (AED), n(%) | |||
  1st quartile (≤ 37,200) | 55(29.4%) | 9(13.2%) | 64(25.1%) |
  2nd quartile (> 37,200– 96,000) | 50 (26.7%) | 21(30.9%) | 71(27.9%) |
  3rd quartile (> 96,000 – 192,000) | 42 (22.5%) | 18(26.5%) | 60(23.5%) |
  4th quartile (> 192,000) | 40 (21.4%) | 20(29.4%) | 60(23.5%) |
Nationality, n(%) | |||
  UAE | 59(31.6%) | 29(42.6%) | 88(34.5%) |
  Non-UAE | 128 (6.4%) | 39(57.4%) | 167(65.5%) |
Disease type, n(%) | Â | Â | Â |
  β-thalassemia major | 172(92.0%) | 59(86.7%) | 231(90.6%) |
  β-thalassemia intermedia | 7(3.7%) | 7(10.3%) | 14(5.5%) |
  Hemoglobin E/β-thalassemia | 7(3.7%) | 1(1.5%) | 8(3.1%) |
  α-thalassemia intermedia | 1(0.5%) | 1(1.5%) | 2(0.8%) |
ICT, n(%) | |||
  DFX | 125(66.8%) | 56(82.4%) | 181(71.0%) |
  DFP | 10(5.3%) | 1(1.5%) | 11(4.3%) |
  DFO | 26(13.9%) | 9(13.2%) | 35(13.7%) |
  Combined therapy | 26(13.9%) | 2(2.9%) | 28(11.0%) |
Ferritin level, n(%) | |||
   < 2000 ng/ml | 70(37.4%) | 25(36.8%) | 95(27.3%) |
   ≥ 2000 ng/ml | 117(62.6%) | 43(63.2%) | 160(62.7%) |
History of splenectomy, n(%) | |||
  No | 162(86.6%) | 67(98.5%) | 229(89.8%) |
  Yes | 25(13.4%) | 1(1.5%) | 26(10.2%) |
Number of complications, n(%) | |||
  No complication | 5(2.7%) | 39(57.4%) | 44(17.2%) |
  One complication | 83(44.4%) | 25(36.8%) | 108(42.4%) |
  Two complications | 69(36.9%) | 4(5.9%) | 73(28.6%) |
  Three or more complications | 30(16.0%) | 0 (0%) | 30(11.8%) |
Cardiac complications, n(%) | |||
  No | 169(90.4%) | 66(97.1%) | 235(92.2%) |
  Yes | 18(9.6%) | 2(2.9%) | 20(7.8%) |
Hepatic complications, n(%) | |||
  No | 146(78.1%) | 67(98.5%) | 213(83.5%) |
  Yes | 41(21.9%) | 1(1.5%) | 42(16.5%) |
Endocrine system complications, n(%) | |||
  No | 85(45.5%) | 57(86.8%) | 142(55.7%) |
  Yes | 102(54.5%) | 11(13.2%) | 113(44.3%) |
Bone complications, n(%) | |||
  No | 35(18.7%) | 47(69.1%) | 82(32.2%) |
  Yes | 152(81.3%) | 21(30.9%) | 173(67.8%) |