Self-efficacy and self-management strategies in acute intermittent porphyria

Table 1 Sociodemographic data and number of participants in the different study groups

Participant characteristics	All (n = 140)	P ^a	Symptomatic			Asymptomatic			Unclassified (n = 6)
Participant characteristics	All (n = 140)	P ^a	Received GC (n = 34)	No GC (n = 72)	p	Received GC (n = 14)	No GC (n = 14)	p	Unclassified (n = 6)
Women (%)	58	0.02	68	64	0.70	21	43	0.23	50
Age, mean (range) in years	52 (18–89)	0.03	51 (20–73)	56 (18–89)	0.10	42 (28–58)	47 (23–82)	0.03	52 (22–66)
Children (%)	79	0.47	79	82	0.76	79	71	0.66	67
Cohabiting status (%)^b		0.36			0.16			0.80
Living alone	21		17	25		14	14		33
Cohabitant	77		79	75		86	79		67
Highest level of education (%)		0.55			< 0.01			0.20
Secondary school			3	33		7	29		33
High school			56	39		36	43		33
College/university			41	28		57	29		33
Occupational status (%)		0.04			0.02			0.39
Employed^c	62		79	47		93	79		33
Pensioner	19		3	31		0	7		33
Disabled	16		18	18		7	14		0
Other	3		0	4		0	0		33

^a Difference between the self-assessed symptomatic (n = 106) and asymptomatic HMBS mutation carriers (n = 28) with categorical variables analysed by χ2 test for independence, and for age by one-way analysis of variance (ANOVA)
^b Data not reported by two persons, one in the symptomatic and one in the asymptomatic group
^c Includes homeworkers and students
Differences were assessed between the symptomatic and asymptomatic group and between the subgroups of those who had reported receiving genetic counseling (GC) or not

ISSN: 1472-6963